Fetus in fetu (FIF) is a rare congenital anomaly. It is a condition in which malformed and parasitic fetus is located in the body of its twin. The anomaly was first defined in early nineteenth century by Meckel.[1,2] Despite its prevalence among infants and children, there have been reports of cases in which the anomaly had remained asymptomatic until later ages.[3–5] This rare congenital anomaly, which was reported around 100 times since its first definition in the nineteenth century, has been discussed with respect to its prognosis and treatment in the light of the relevant literature.